The International Center for Nephrogenic Systemic Fibrosis Research (ICNSFR)


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Article Summaries

Realizing that most patients (and many doctors) do not have the same level of access to the medical literature that I have on this subject, below is my attempt to summarize, chronologically, the articles published on NFD/NSF. This is necessarily a "subjective" exercise on my part -- as are all "editorial" exercises. Please keep this in mind as you read. Important "discoveries" are in bold, and personal editorial comments are inserted when I judge these need to be made (these are recognized as having a blue colored font). Also, an ongoing working hypothesis is indicated in red. NFD should be considered an equivalent terminology to NFD/NSF.


Article 1
September 2000

Cowper SE, Robin HS, Steinberg SM, Su LD, Gupta S, LeBoit PE. Scleromyxoedema-like cutaneous disease in renal-dialysis patients. The Lancet 2000; 356(9234):1000-1
PubMed Abstract


Article 2
October 2001

Cowper SE, Su L, Robin H, Bhawan J, LeBoit PE. Nephrogenic Fibrosing Dermopathy. Amer J Dermatopathol 2001; 23(5): 383-393
PubMed Abstract


Article 3
January 2002

Fibrosing skin condition among patients with renal disease—United States and Europe 1997-2002. MMWR/Morb Mortal Wkly Rep 2002; 51:25-6
Link to article


Article 4
June 2002

McNeill AM, Barr RJ. Scleromyxedema-like fibromucinosis in a patient undergoing hemodialysis. Int J Dermatol 2002; 41(6): 364-7
PubMed Abstract


Article 5
September 2002

Bates B. New Dermopathy Seen in Kidney Disease Patients. eSkin and Allergy News 2002; 33(9)
Link to article (free registration)


    Article 6
    January 2003

    Bardin T. Musculoskeletal manifestations of chronic renal failure. Curr Opin Rheumatol 2003; 15(1): 48-54
    PubMed Abstract


    Article 7
    January 2003

    Mackay-Wiggan JM, Cohen DJ, Hardy MA, Knobler EH, Grossman ME. Nephrogenic fibrosing dermopathy (scleromyxedema-like illness of renal disease). Jour Amer Acad Dermatol 2003; 48(1): 55-60
    PubMed Abstract


    Article 8
    January 2003

    Streams BN, Liu V, Liegeois N, Moschella SM. Clinical and pathological features of nephrogenic fibrosing dermopathy. Jour Amer Acad Dermatol. 2003; 48(1): 42-7
    PubMed Abstract


    Article 9
    March 2003

    Hubbard V, Davenport A, Jarmulowicz M, Rustin M. Scleromyxoedema-like change in four renal dialysis patients. Br J Dermatol. 2003; 148(3): 563-8
    PubMed Abstract


    Article 10
    May 2003

    Swartz RD, Crofford LJ, Phan SH, Ike RW, Su LD. Nephrogenic Fibrosing Dermopathy: A novel cutaneous fibrosing disorder in patients with renal failure. Am J Med. 2003; 114(7): 563-72
    PubMed Abstract


    Article 11
    May-June 2003

    Ishibe S, Perazella MA, Reilly RF. Nephrogenic Fibrosing Dermopathy: an unusual skin condition associated with kidney disease. Semin Dial. 2003; 16(3): 276-80
    PubMed Abstract


    Article 12
    June 2003

    Baron PW, Cantos K, Hillebrand DJ, H KQ, Ojogho ON, Nehlsen-Cannarella S, Concepcion W. Nephrogenic Fibrosing Dermopathy After Liver Transplantation Successfully Treated With Plasmapheresis. Amer J Dermatopathol 2003; 25(3):204-209
    PubMed Abstract


    Article 13
    July 2003

    Ting WW, Stone MS, Madison KC, Kurtz K. Nephrogenic Fibrosing Dermopathy with Systemic Involvement. Archiv Dermatol 2003; 139(7):903-6
    PubMed Abstract


    Article 14
    July 2003

    Leboit PE. What nephrogenic fibrosing dermopathy might be. Archiv Dermatol 2003; 139(7):928-30
    PubMed Abstract


    Article 15
    August 2003

    Cowper SE, Bucala R. Nephrogenic Fibrosing Dermopathy: Suspect Identified, Motive Unclear.[Letter] Amer J Dermatopathol 2003; 25(4):358
    PubMed Abstract


    Article 16
    October 2003

    Hancox JG, Mengesha YM, Sangueza OP, Yosipovitch G. Nephrogenic fibrosing dermopathy after five days of hemodialysis. J Drugs Dermatol. 2003; 2(5):550-3
    PubMed Abstract


    Article 17
    November 2003

    Cowper SE. Nephrogenic Fibrosing Dermopathy: The First Six Years. Curr Opin Rheumatol. 2003;15(6):785-90
    PubMed Abstract


    Article 18
    November 2003

    Jan F, Segal JM, Dyer J, Leboit P, Siegfried E, Frieden IJ. Nephrogenic Fibrosing Dermopathy: Two Pediatric Cases. J Pediatr. 2003; 143:678-81
    PubMed Abstract


    Article 19
    December 2003

    Engelen JW, Kooistra MP, Canninga-van Dijk MR, Toonstra J, Sigurdsson V. Nephrogenic Fibrosing Dermopathy [Dutch] 2003; Ned Tijdschr Geneeskd. 147(49):2435-8
    PubMed Abstract


    Article 20
    January 2004

    Dawn G, Holmes SC. Scleromyxoedema-like eruption following haemodialysis or Nephrogenic Fibrosing Dermopathy? [Letter] 2004; Br J Dermatol. 150(1):167-8
    PubMed Abstract


    Article 21
    February 2004

    Evenepoel P, Zeegers M, Segaert S, Claes K, Kuypers D, Maes B, Flamen P, Fransis S, Vanrenterghem Y. Nephrogenic Fibrosing Dermopathy: A Novel Disabling Disorder in Patients with Renal Failure. Nephrol Dial Transplant. 2004; 19(2):469-73
    PubMed Abstract


    Article 22
    February 2004

    Jain SM, Wesson S, Hassanein A, Canova E, Hoy M, Fennell RS, Dharnidharka VR. Nephrogenic Fibrosing Dermopathy in pediatric patients. Pediatr Nephrol. 2004; 19(4):467-70
    PubMed Abstract


    Article 23
    March 2004

    Edsall LC, English JC, Patterson JW. Calciphylaxis and metastatic calcification associated with nephrogenic fibrosing dermopathy. J Cutan Pathol. 2004; 31(3):247-53
    PubMed Abstract


    Article 24
    March 2004

    Hershko K, Hull C, Ettefagh L, Nedorost S, Dyson S, Horn T, Gilliam AC. A variant of nephrogenic fibrosing dermopathy with osteoclast-like giant cells: a syndrome of dysregulated matrix remodelling? J Cutan Pathol. 2004; 31(3):262-5
    PubMed Abstract


    Article 25
    March 2004

    Chiu H, Wells G, Carag H, Canova E, Firpi RJ. Nephrogenic fibrosing dermopathy: A rare entity in patients awaiting liver transplantation Liver Transpl. 2004; 10(3):465-6
    PubMed Abstract


    Article 26
    March 2004

    Chung HJ, Chung KY. Nephrogenic fibrosing dermopathy: response to high-dose intravenous immunoglobulin [Letter] Br J Dermatol. 2004; 150(3):596-7
    PubMed Abstract


    Article 27
    April 2004

    Quan TE, Cowper S, Wu SP, Bockenstedt LK, Bucala R. Circulating fibrocytes: Collagen-secreting cells of the peripheral blood. Int J Biochem Cell Biol. 2004; 36(4):598-606
    PubMed Abstract


    Article 28
    May 2004

    Gambichler T, Paech V, Kreuter A, Wilmert M, Altmeyer P, Stucker M. Nephrogenic fibrosing dermopathy. Clin Exp Dermatol. 2004; 29(3):258-60
    PubMed Abstract


    Article 29
    May 2004

    Lauchli S, Zortea-Caflisch C, Nestle FO, Burg G, Kempf W. Nephrogenic fibrosing dermopathy treated with extracorporeal photopheresis. Dermatology 2004; 208(3):278-80
    PubMed Abstract


    Article 30
    May 2004

    Ortonne N, Lipsker D, Chantrel F, Boehm N, Grosshans E, Cribier B. Presence of CD45RO+ CD34+ cells with collagen synthesis activity in nephrogenic fibrosing dermopathy: a new pathogenic hypothesis [Letter] Br J Dermatol. 2004; 150(3):1050-2
    PubMed Abstract


    Article 31
    July 2004

    Hauser C, Kaya G, Chizzolini C. Nephrogenic fibrosing dermopathy in a renal transplant recipient with tubulointerstitial nephritis and uveitis. Dermatol. 2004; 209(1):50-2
    PubMed Abstract


    Article 32
    July 2004

    Tan AW, Tan SH, Lian TY, Ng SK. A case of nephrogenic fibrosing dermopathy. Ann Acad Med Singapore. 2004; 33(4):527-9
    PubMed Abstract


    Article 33
    August 2004

    Jimenez SA, Artlett CM, Sandorfi N, Derk C, Latinis K, Sawaya H, Haddad R, Shanahan JC. Dialysis-associated systemic fibrosis (nephrogenic fibrosing dermopathy): study of inflammatory cells and transforming growth factor beta1 expression in affected skin. Arthritis Rheum. 2004; 50(8):2660-6
    PubMed Abstract


    Article 34
    August 2004

    Taylor EN, Henderson JM, Rennke HG, Magee CC. Traumatic calcinosis cutis in a dialysis patient. Am J Kidney Dis. 2004; 44(2):e6-9
    PubMed Abstract

    Coming soon!


    Article 35
    August 2004

    Obermoser G, Emberger M, Wieser M, Zelger B. Nephrogenic fibrosing dermopathy in two patients with systemic lupus erythematosus. Lupus. 2004; 13(8):609-12
    PubMed Abstract


    Article 36
    November 2004

    Levine JM, Taylor RA, Elman LB, Bird SJ, Lavi E, Stolzenberg ED, McGarvey ML, Asbury AK, Jimenez SA. Involvement of skeletal muscle in dialysis-associated systemic fibrosis (nephrogenic fibrosing dermopathy). Muscle Nerve. 2004; 30(5):569-77
    PubMed Abstract


    Article 37
    November 2004

    Gremmels JM, Kirk GA. Two Patients With Abnormal Skeletal Muscle Uptake of Tc-99m Hydroxymethylene Diphosphonate Following Liver Transplant: Nephrogenic Fibrosing Dermopathy and Graft vs Host Disease. Clin Nucl Med. 29(11):694-7.
    PubMed Abstract

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